Summary

Congenital coronary artery anomalies are rare, with an incidence of about 0.3% to 1.3% of all patients undergoing cardiac angiography. Although many anomalies are asymptomatic and benign, more serious defects can cause significant morbidity and mortality. The structure of the anomalous vessel, particularly its origin and course, often determines patient prognosis. This article discusses contemporary options for imaging and revascularization in patients with ACAOS.