Summary

Pulmonary arterial hypertension (PAH) is a rare cardiopulmonary disease that is associated with remodeling within the small pulmonary arteries, increased pulmonary vascular resistance, and right ventricular failure. Identifying PAH is a challenge for clinicians, in part due to its nonspecific symptoms, such as dyspnea, chest pain, heart failure, and palpitations. As a result, the accurate diagnosis of PAH is often delayed up to 2 years after symptom onset. This article describes the role of new imaging technology in improving the diagnosis and assessment of patients with PAH.